CASE REPORT Colonic angiomyolipoma with a monotypic expression and a predominant epithelioid component
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چکیده
Angiomyolipomas are rare lesions, often arising in the kidney, and are part of a group of tumours with a diverse appearance and evidence of dual melanocytic and smooth muscle differentiation known as PEComas (tumours of perivascular epithelioid cell origin). This report describes an unusual case of a colonic PEComa in a 40 year old woman. Unlike most of the previous colonic angiomyolipomas/ PEComas reported in the literature, this case formed a large, mainly extrinsic mass and was monotypic, and composed entirely of the myomatous component with no adipose tissue or typical vasculature.
منابع مشابه
Colonic angiomyolipoma with a monotypic expression and a predominant epithelioid component.
Angiomyolipomas are rare lesions, often arising in the kidney, and are part of a group of tumours with a diverse appearance and evidence of dual melanocytic and smooth muscle differentiation known as PEComas (tumours of perivascular epithelioid cell origin). This report describes an unusual case of a colonic PEComa in a 40 year old woman. Unlike most of the previous colonic angiomyolipomas/PECo...
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Perivascular epithelioid cells (PECs) were initially proposed, by Bonetti et al. in 1992, to describe an “unusual atypical cell type” of epithelioid shape and harboring a clear to eosinophilic cytoplasm with perivascular distribution in both renal angiomyolipoma (AML) and clear cell sugar tumor (CCST) of the lung. This perception gradually became accepted and led to the concept of perivascular ...
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